منابع مشابه
Modeling alveolar capillary dysplasia.
To the Editor, I read with great interest the article by Han et al,1 who studied lung morphology in developing endothelial NO synthase (eNOS)deficient mice. The authors presented exciting data on defective peripheral lung vessel development, which was combined with impaired alveolar maturation. These data reflect very well the current thinking of lung development regulated by molecular cross-ta...
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Alveolar capillary dysplasia with misalignment of the pulmonary veins (ACD/MPV) is a rare, fatal developmental lung disorder of neonates and infants. This review aims to address recent findings in the etiology and genetics of ACD/MPV and to raise awareness of this poorly known disease, which may also present as milder, unclassified forms. Successively discussed are what is known about the epide...
متن کاملAlveolar capillary dysplasia with anorectal anomaly.
Alveolar capillary dysplasia (ACD) is an uncommon cause of irreversible persistent pulmonary hypertension in full-term newborn. In ACD there is a failure of formation of air - blood barrier in addition to misalignment of pulmonary veins. The etiology of the disease is still not understood. We present a case report of a full-term newborn with ACD associated with anorectal anomaly.
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Alveolar capillary dysplasia (ACD) is a congenital, lethal disorder of the pulmonary vasculature. Phosphatase and tensin homologue deleted from chromosome 10 (Pten) encodes a lipid phosphatase controlling key cellular functions, including stem/progenitor cell proliferation and differentiation; however, the role of PTEN in mesodermal lung cell lineage formation remains unexamined. To determine t...
متن کاملAlveolar Capillary Dysplasia with Misalignment of Pulmonary Veins (ACD/MPV): A Case Series
Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a rare, fatal, developmental lung disorder, which usually presents as persistent pulmonary hypertension of the newborn (PPHN) unresponsive to treatment. The authors present their own experience with three cases admitted during the last 15 years.
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ژورنال
عنوان ژورنال: American Journal of Respiratory and Critical Care Medicine
سال: 2011
ISSN: 1073-449X,1535-4970
DOI: 10.1164/rccm.201010-1697ci